Zinner Syndrome: A Rare Cause of Chronic Pelvic Pain in a Male Patient — Case Report

Author(s): Giovanni Vitor Garabini, Matheus Naves Rosa, Fernando Aparecido Pazini, Guilherme Ribeiro de Mendonça Gonçalves Da Silva, Daniel Salermo Muzilli, Mateus Santos Matos, Laiane Milani de Arruda, Thiago da Silveira Antoniassi

Zinner syndrome is an uncommon congenital malformation of the male genitourinary tract defined by the triad of unilateral renal agenesis, seminal vesicle cyst, and ipsilateral ejaculatory duct obstruction. A case report a 39-year-old man with a one-year history of intermittent right iliac fossa pain without urinary or reproductive complaints. Clinical evaluation and magnetic resonance imaging demonstrated right renal agenesis, multiple seminal vesicle cysts, and dilatation of the right ejaculatory duct, establishing the diagnosis. The patient was managed conservatively with outpatient follow-up and analgesia, with subsequent improvement of symptoms. This case highlights the pivotal role of MRI in precise anatomic characterization and diagnostic confirmation of Zinner syndrome and emphasizes that treatment should be individualized according to symptom burden, ranging from observation to minimally invasive surgical intervention in refractory or complicated presentations.

Zinner Syndrome, Renal Agenesis, Seminal Vesicle Cyst, Ejaculatory Duct Obstruction, Mesonephric Duct Anomaly, Magnetic Resonance Imaging, Male Infertility, Minimally Invasive Surgery

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